| Introduction: | | | | Fifty percent of sarcoid cases have clinically silent |
| Sarcoidosis with a prevalence of 10/100,000, is a | | | | involvement of organs, which is one of the |
| multisystem disease of unknown etiology | | | | hallmarks.¹ 20-40% of symptomatic patients |
| characterized by non-caseating granulomas.i It | | | | have respiratory symtoms and 10-40% have eye |
| involves virtually any organ, lungs, thoracic lymph | | | | pain, rashes arthralgia and other symptoms while |
| nodes, skin liver, central nervous system, eyes, | | | | 20-30% with constitutional symptoms like weight loss |
| kidneys and heart, and is more common in | | | | and fatigue.¹ |
| Afro-Americans. There is no sex predilection but | | | | Sarcoidosis may present atypically as Lofgrens and |
| some manifestations of the disease are more | | | | HeerFordts syndrome.¹ Sarcoidosis in younger |
| common is females. ² It begins in the third or | | | | patients with spontaneous remission and less than |
| fourth decade and tends to be rare in children and | | | | two years duration of symptoms are classified as |
| the elderly.? We are presenting a case of sarcoidosis | | | | subacute while chronic form have more than two |
| of the lungs which should be considered in the | | | | years duration with insidious onset and presents with |
| differential diagnosis of tuberculosis, common in | | | | constitutional symptoms, pulmonary fibrosis and |
| countries like Pakistan. | | | | nephrocalcinosis.¹ |
| Discussion: | | | | In one study in which histopathological diagnosis |
| Considering the common disease first which is | | | | required presence of non-caseating granuloma, |
| tuberculosis, long-standing history of low grade fever, | | | | bronchoscopic biopsy yielded diagnosis in 60% of |
| weight loss and persistent cough not responding to | | | | patients with stage I disease, tranbronchial needle |
| anitibiotics along with raised ESR and positive PPD(13 | | | | aspiration yielded diagnosis in 53% and two |
| mm) supports tuberculosis put PPD is not reliable in | | | | procedures in combination yielded 83% of diagnosis. |
| developing countries as a tool for diagnosis. | | | | 7,8 In stage II disease probability of obtaining a |
| Diagnostic procedure performed was an | | | | positive result with a single specimen was 46%, the |
| endobronchial biopsy. ² Histopathological | | | | yielded with more specimens followed a logarithmic |
| examination showed multiple granulomas, composed | | | | curve and increased to 90% with four specimen, at |
| of epitheloid histiocytes, with occasional Langerhans | | | | which point the yield approached a plateau for |
| giant cell and no necrosis. According to one study | | | | additional specimen. 7,8 The suggests that four |
| endobronchial biopsy increased the yield of fibreoptic | | | | biopsy specimens are sufficient to make diagnosis. |
| bronchoscopy by 20.6%.4 Fungal stain, AFB stains | | | | Biopsy of gastrocnemius muscle is another sensitive |
| and cultures, were negative (Table II). | | | | and specific tool for diagnosis. 9 If transbronchial |
| The patient had X-ray findings consistent with stage | | | | biopsies are non-diagnostic, mediastinal lymph node |
| II disease. 1,5 Unilateral hilar adenopathy is an atypical | | | | biopsies are diagnostic in 8-90% of case. 10 Finally , |
| manifestation of sarcoidosis in initial stage. 6 Her ACE | | | | the patient was kept on steroids (Deltacortil) 40mg |
| level was raised about three folds, serum calcium was | | | | day in divided doses and He/She responded well with |
| in upper normal range and ESR was persistently | | | | remarkable improvements. 11 His/Her ESR came |
| raised (Table I) supported by radiological findings, | | | | down to 13mm, chest X-ray showed remarkable |
| which favour sarcoidosis. PPD is negative in | | | | improvement as infiltrates and bilateral hilar |
| sarcoidosis are anergic to PPD tuberculin but | | | | adenopathy disappeared altogether. |
| distribution of memory T-cells in the blood and | | | | We kept His/Her on the same dose of Deltacortil till |
| humoral immune response are normal and | | | | 8 weeks, and then it was trapered off to 7.5mg/day |
| opportunistic infections are rare.¹ | | | | without recurrence. |